Gorham Stout disease of the temporal bone with cerebrospinal fluid leak

xlomafota13 shared this article with you from Inoreader Gorham Stout disease of the temporal bone with cerebrospinal fluid leak Via leak of cerebrospinal fluid Childs Nerv Syst. 2021 Jun 11. doi: 10.1007/s00381-021-05245-1. Online ahead of print. ABSTRACT Gorham Stout disease (GSD) is a rare disease characterized by the proliferation of endothelial lined vessels and replacement of bone by fibrous tissue. The main imaging features are progressive osteolysis and cortical resorption. Temporal bone involvement is rare but presents as a destructive bone lesion that may be misinterpreted as more common lytic processes in the pediatric population, such as infection or Langerhans cell histiocytosis. GSD of the temporal bone is associated with cerebrospinal fluid (CSF) leaks, may present with otorrhea, and can mimic other causes of ear drainage. Here, we report the clinical course, imaging features, and outcomes of a 3-year-old girl with GSD of the temporal bone presenting with CSF leak initially attributed to infection. PMID:34115176 | DOI:10.1007/s00381-021-05245-1 View on the web Inoreader. Take back control of your news feed. Follow us on Twitter and Facebook.