Cerebrospinal fluid-lymphatic fistula causing spontaneous intracranial hypotension in a child with kaposiform lymphangiomatosis

xlomafota13 shared this article with you from Inoreader Cerebrospinal fluid-lymphatic fistula causing spontaneous intracranial hypotension in a child with kaposiform lymphangiomatosis Via leak of cerebrospinal fluid Pediatr Radiol. 2021 Jul 20. doi: 10.1007/s00247-021-05132-6. Online ahead of print. ABSTRACT Spontaneous intracranial hypotension is an uncommon etiology of secondary headaches in children. We report a unique case of a girl with kaposiform lymphangiomatosis who developed postural headaches and imaging features of spontaneous intracranial hypotension without a spinal extradural collection. The girl underwent dynamic computed tomography myelography which revealed a cerebrospinal fluid (CSF)-lymphatic fistula related to a lymphatic malformation associated with the right T10 nerve. She underwent surgical ligation of the CSF-lymphatic fistula, resulting in resolution of the headaches. Spinal CSF-lymphatic fistulas are rare and have previously been reported in two patients with Gorham-Stout disease. The current report suggests that patients with systemic lymphatic anomalies who develop postural headaches should undergo evaluation for spontaneous i ntracranial hypotension and a CSF-lymphatic fistula. If discovered, surgical ligation is a potential treatment. PMID:34286352 | DOI:10.1007/s00247-021-05132-6 View on the web Inoreader. Take back control of your news feed. Follow us on Twitter and Facebook.